Choledocal Cysts

Last updated 20.09.12

 

Definition

-  Congenital disorder of biliary tree with cystic dilation &/or cyst formation

Features

-  Types I to V

-  Type I 80-90%

-  Saccular or fusiform dilation of entire common hepatic & bile ducts or segments

-  Most common

 

Associated S/S

-  May present at any age

-  67% prior to 10yrs old

-  Infants: jaundice, acholic stools +/- hepatomegaly

-  Recurrent acute pacreatitis

-  Adults: RUQ pain

-  Associated with biliary atresia

-  Premalignancy --> carcinoma therefore surgery

 

Ix

-  Abdominal ultrasound

-  +/- CT or MRI or MRCP

 

Mx

-  Surgery: Laparoscopic

-  Type I: complete excision +

-  Roux-en-Y biliary enteric anastomosis

-  Modified Kasai procedure

 

 

 

References